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What is Hemophilia?

Haemophilia is a rare, genetic condition which prevents the blood from clotting. This causes excessive bleeding even in minor injuries and sometimes internally without even injury. It is also called bleeder’s disease.

What are its main signs and symptoms?

Haemophiliaprevents the blood from clotting normally. Haemophilia patients may bleed for a longer time than others after an injury which can lead to death due to excessive loss of blood if not immediately attended to medically.

  • Signs of external bleeding
    • Bleeding in the mouth
    • Heavy bleeding from a small cut
    • Nose bleeding
  • Signs of internal bleeding
    • Blood in the urine and stool Read more: Blood in urine causes
    • Large bruises from bleeding over the large muscles of the body
    • Bleeding in the joints without any injury
    • Bleeding in the brain after a minor bump on the head or more serious injury

What are its causes?

Haemophilia patients lack a necessary enzyme called thromboplastin due to which blood coagulation is impaired in these people. It mostly affects boys because it is an X-linked genetic trait. A hemophilic girl most often dies before birth itself.

There are two types of haemophilia:

  • Hemophilia A
    • It is characterised by lack of antihemophilic globulin (factor VII).
    • About four-fifths of the cases of haemophilia are of this type.
    • It is more severe.
    • Therefore, even a very small cut may lead to continuous bleeding for a long time.
  • Hemophilia B
    • It is also known as Christmas disease.
    • It results from a defect in plasma thromboplastin component  (PTC or Factor IX).

How is it diagnosed and treated?

Diagnosis is made by a genetic testing which is followed by genetic counselling. Being a genetic condition, haemophilia cannot be cured. Since the main goal is to prevent joint bleeding and its complications, urgent medical management for persons with severe haemophilia A and B should be provided. Episodes of bleeding in haemophilia patients require Factor VII or Factor IX replacement therapy.

  • Improved screening of blood and plasma donors have resulted in safer plasma-derived Factor VII and Factor IX concentrates.
  • For persons with haemophilia A, viral safety should be the primary criterion for choosing between available blood transfusion products.
  • For persons with mild or moderate haemophilia A, DDAVP should be used whenever appropriate.
  • For persons with haemophilia B, high purity Factor IX concentrates should be used in specific circumstances to help blood clotting. In all other situations, the use of prothrombin complex concentrates can be considered as well.
  • Surgery involving patients with haemophilia should only be undertaken after sufficient supplies of the necessary therapeutic products are available to cover the operative and post-operative periods. Such procedures require close cooperation between the physician, the blood bank or pharmacy, the surgeon and coagulation laboratory personnel.

(Read more: Blood clotting disorders types)

  1. Medicines for Hemophilia

Medicines for Hemophilia

Medicines listed below are available for Hemophilia. Please note that you should not take any medicines without doctor consultation. Taking any medicine without doctor's consultation can cause serious problems.

Medicine NamePack SizePrice (Rs.)
EmsylEmsyl 250 Mg Tablet56.0
ClipClip 500 Mg Injection39.0
CyklokapronCyklokapron 500 Mg Injection191.0
PausePause 1000 Mg Tablet239.0
TexakindTexakind 500 Mg Injection35.0
TranesmaTranesma 250 Mg Tablet199.0
TranostatTranostat 500 Mg Injection69.0
TrapicTrapic 100 Mg Injection68.0
Trenaxa TabletTrenaxa 1000 Mg Tablet128.0
XamicXamic 500 Mg Injection69.0
AtsyteAtsyte 500 Mg Injection80.0
CeltranzCeltranz 500 Mg Injection54.0
Clotawin TClotawin T 100 Mg Injection34.0
Clot PlusClot Plus Tablet140.0
Clot XlClot Xl 500 Mg Injection41.0
CoastatCoastat 100 Mg Injection45.0
Cosklot TCosklot T 500 Mg Injection60.0
ExtamExtam 500 Mg Tablet49.0
GlantraxGlantrax 500 Mg Injection69.0
Inmela (Veritaz)Inmela 250 Mg Tablet189.0
KlotinKlotin 100 Mg Injection63.0
MenogiaMenogia 500 Mg Injection70.0
NexamicNexamic 500 Mg Tablet116.0
Nexna TxNexna Tx Tablet140.0
NolossNoloss 500 Mg Tablet123.0
ProklotProklot 500 Mg Tablet11.0
StopbleedStopbleed 500 Mg Injection85.0
SynostatSynostat 500 Mg Injection45.0
TenacidTenacid 500 Mg/5 Ml Injection23.0
TexidTexid 500 Mg Injection62.0
TraclotTraclot 500 Mg Tablet114.0
TraklotTraklot 500 Mg Injection30.0
TramixTramix 500 Mg Injection66.0
TranceTrance 500 Mg Injection43.0
TranecidTranecid 500 Mg Injection58.0
TranemicTranemic 500 Mg Injection39.0
Tranesma PlusTranesma Plus Tablet229.0
TranlokTranlok 500 Mg Injection50.0
TranomacTranomac 500 Mg Tablet101.0
TraxageTraxage 250 Mg Tablet140.0
TrexanetTrexanet 500 Mg Tablet130.0
BleenaBleena Injection48.0
CutiCuti 500 Mg Injection30.0
CyminCymin 250 Mg Capsule72.0
Derma RadiaDerma Radia Tablet265.0
DesqualDesqual M Tablet179.0
DubatranDubatran 10 Mg Tablet100.0
FudartFudart 500 Mg Tablet130.0
Gynae PilGynae Pil 500 Mg Tablet25.0
HexamicHexamic Injection39.0
KomelaKomela 250 Mg Tablet120.0
NexiNexi Injection39.0
NobleedNobleed 500 Mg Tablet160.0
PauseraPausera 500 Mg Tablet157.0
TanmicTanmic 500 Mg Tablet53.0
TenexaTenexa 500 Mg Injection46.0
TraneeTranee 500 Mg Injection28.0
TranemolTranemol 500 Mg Injection49.0
TransolTransol 500 Mg Tablet105.0
TranxiTranxi 250 Mg/250 Mg Tablet110.0
WistranWistran 500 Mg Injection27.0
Agretax MfAgretax Mf 500 Mg/250 Mg Tablet61.54
Biostat MfBiostat Mf Tablet130.0
ChromostatChromostat Injection8.5
Clot Xl MClot Xl M 500 Mg/250 Mg Tablet218.0
Cosklot MfCosklot Mf 500 Mg/250 Mg Tablet195.0
Din TmDin Tm 500 Mg/250 Mg Tablet96.25
Emsyl TmEmsyl Tm 500 Mg/250 Mg Tablet160.0
Etosys MfEtosys Mf 500 Mg/250 Mg Tablet96.0
EvastatEvastat 500 Mg/250 Mg Tablet82.0
FemidolFemidol 500 Mg/250 Mg Tablet31.83
Fibrinil MfFibrinil Mf 500 Mg/250 Mg Tablet144.32
Kenex MfKenex Mf 500 Mg/500 Mg Tablet149.0
MefatranMefatran Tablet160.0
Mefcid TaMefcid Ta 250 Mg/500 Mg Tablet129.0
MeftranMeftran 500 Mg/250 Mg Tablet142.86
Nexi MNexi M 500 Mg/250 Mg Tablet125.0
Noloss MfNoloss Mf Tablet139.55
OrsikOrsik Tablet40.0
Orsik TmOrsik Tm Tablet119.05
RapicogRapicog 500 Mg/250 Mg Tablet199.0
Rapicog DsrRapicog Dsr Capsule99.1
Rapicog LsRapicog Ls Capsule127.0
Sofia TmSofia Tm 500 Mg/250 Mg Tablet275.0
Synostat MfSynostat Mf 500 Mg/250 Mg Tablet136.71
Taxi MfTaxi Mf 500 Mg/250 Mg Tablet220.01
Texid MfTexid Mf Tablet201.0
TmTm 500 Mg/250 Mg Tablet188.57
Traclot MfTraclot Mf 500 Mg/250 Mg Tablet80.0
Traklot MfTraklot Mf 500 Mg/250 Mg Tablet109.71
Tramed PTramed P 500 Mg/250 Mg Tablet28.0
Trance MfTrance Mf 500 Mg/250 Mg Tablet140.0
Tranecid MfTranecid Mf 500 Mg/250 Mg Tablet161.91
Trapic MfTrapic Mf Tablet252.0
Traxage MfTraxage Mf 500 Mg/250 Mg Tablet140.0
Traxel MfTraxel Mf 500 Mg/250 Mg Tablet109.0
Trenaxa MfTrenaxa Mf 500 Mg/250 Mg Tablet165.0
Trexanet MfTrexanet Mf 500 Mg/250 Mg Tablet150.0
Tx MfTx Mf 500 Mg/250 Mg Tablet86.53
Xamic MfXamic Mf 500 Mg/250 Mg Tablet204.0
Bleena MfBleena Mf 500 Mg/250 Mg Tablet105.6
Clip MfClip Mf 500 Mg/250 Mg Tablet108.0
ClostopClostop Sr 500 Mg/250 Mg Tablet250.0
Clotawin MfClotawin Mf 500 Mg/250 Mg Tablet200.0
ConrageConrage 500 Mg/250 Mg Tablet94.92
Cuti MCuti M 500 Mg/250 Mg Tablet144.37
Cyclosym Tx TabletCyclosym Tx Tablet14.02
Cymin MfCymin Mf 500 Mg/250 Mg Tablet98.2
DubaceDubace Tablet230.0
Dubatran MfDubatran Mf 500 Mg/250 Mg Tablet60.91
Evetra MfEvetra Mf 500 Mg/250 Mg Tablet82.32
ExamicExamic 500 Mg/250 Mg Tablet177.0
Gynae Pil ForteGynae Pil Forte 500 Mg/250 Mg Tablet149.75
Mck M PlusMck M Plus 500 Mg/250 Mg Tablet117.05
Mefalth TMefalth T 500 Mg/250 Mg Tablet85.57
MefnoxMefnox Tablet99.95
Meftal TxMeftal Tx Tablet96.0
MeftarisMeftaris Tablet187.0
Menospan MfMenospan Mf 250 Mg/500 Mg Tablet89.0
Nestran MfNestran Mf 500 Mg/250 Mg Tablet126.0
Nobleed TmNobleed Tm 500 Mg/250 Mg Tablet212.5
Pausera MPausera M 500 Mg/250 Mg Tablet190.0
Plug MfPlug Mf 500 Mg/250 Mg Tablet100.0
Rheonex MfRheonex Mf 500 Mg/250 Mg Tablet72.0
Stopbleed TmStopbleed Tm Tablet183.5
Tandem MTandem M 500 Mg/250 Mg Tablet136.6
Tenacid MfTenacid Mf Tablet175.0
Texanam MfTexanam Mf Tablet69.37
Texawock MfTexawock Mf Tablet85.0
TmfTmf 500 Mg/250 Mg Tablet115.37
Tmt (Bestochem)Tmt Tablet119.9
Trafix MfTrafix Mf 500 Mg/250 Mg Tablet190.0
TrafnicTrafnic Tablet156.2
Tragen MfTragen Mf Tablet160.76
Tranarest MfTranarest Mf 500 Mg/250 Mg Tablet133.37
TrandacTrandac 500 Mg/250 Mg Tablet133.18
Tranemol MfTranemol Mf 500 Mg/250 Mg Tablet150.0
Tranex MTranex M Tablet139.0
Tranfib MfTranfib Mf 500 Mg/250 Mg Tablet70.95
Tranlok MTranlok M 500 Mg/250 Mg Tablet161.75
Tranofast MfTranofast Mf Tablet235.0
Transol MfTransol Mf 500 Mg/250 Mg Tablet84.0
Trantas MfTrantas Mf Tablet162.0
Tranxi MTranxi M Tablet145.0
TrapauzTrapauz 500 Mg/250 Mg Tablet132.4
Traxz MTraxz M Tablet67.35
Tugyna MfTugyna Mf 500 Mg/250 Mg Tablet160.0
ZaxidZaxid Tablet132.37
Coastat PlusCoastat Plus 500 Mg/250 Mg Tablet100.57
Cosklot PlusCosklot Plus 250 Mg/250 Mg Tablet143.3
Etex TEtex T 250 Mg/250 Mg Tablet155.0
EthatolEthatol 250 Mg/250 Mg Tablet120.0
EtosysEtosys 250 Mg/250 Mg Tablet138.0
Fibran PlusFibran Plus 250 Mg/250 Mg Tablet150.0
HemoclotHemoclot 250 Mg/250 Mg Tablet18.7
HemocratHemocrat 250 Mg/250 Mg Tablet148.0
KlotranKlotran 250 Mg/250 Mg Tablet152.0
K Stat EtK Stat Et 250 Mg/250 Mg Tablet114.6
Noloss EtNoloss Et Tablet158.8
NosylateNosylate 500 Mg/250 Mg Tablet225.0
RhaginylRhaginyl Tablet125.0
Sylstep TxSylstep Tx 250 Mg/250 Mg Tablet112.5
TheolateTheolate 250 Mg/250 Mg Tablet44.75
Trance EtTrance Et 250 Mg/250 Mg Tablet115.0
TraxylateTraxylate 250 Mg/250 Mg Tablet230.0
Cetham TxCetham Tx 250 Mg/250 Mg Tablet132.0
CoglanCoglan 250 Mg/250 Mg Tablet100.0
E Sylate ME Sylate M 250 Mg/250 Mg Tablet85.56
E Sylate TE Sylate T 250 Mg/250 Mg Tablet209.0
Ethasyl TEthasyl T 500 Mg/250 Mg Tablet152.0
Ethetran PlusEthetran Plus 250 Mg/250 Mg Tablet140.0
HemclotHemclot Tablet161.9
KlatKlat 250 Mg/250 Mg Tablet134.98
ManoguardManoguard 250 Mg/250 Mg Tablet138.08
MenoguardMenoguard 250 Mg/250 Mg Tablet159.5
MenolateMenolate Tablet18.97
Sylate TSylate T 250 Mg/250 Mg Tablet235.4
Syl PlusSyl Plus Tablet150.0
Sylron TxSylron Tx 250 Mg/250 Mg Tablet152.0
Tranlok ETranlok E 500 Mg/250 Mg Tablet164.0
Trapic ETrapic E 250 Mg/250 Mg Tablet177.0
Gse+TxGse+Tx Tablet155.0
TyrodinTyrodin 75 Mg/250 Mg Tablet90.0
Melano TxMelano Tx Cream297.0
PraxamicPraxamic 75 Mg/250 Mg Tablet160.0

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